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Table 1 Fourteen poorly differentiated or undifferentiated cancers identified from hospital pathology records over 26 years

From: Incidence of NUT carcinoma in Western Australia from 1989 to 2014: a review of pediatric and adolescent cases from Perth Children’s Hospital

Patient Case

Age at diagnosis

Gender

Pathology

Tumor site (primary)

Chemo Therapya

Radio therapyb

NUTM1 staining

Diagnosis

Alive

Time to death

1

13 yrs. 9 mo

M

Undifferentiated CA

Nasopharynx

CP

Y (C)

Neg

NPC

Yes

 

2

11 yrs. 7 mo

F

Undifferentiated CA

Mediastinum

Ifos

Y (E)

Pos

NC

No

4.5 Mo

3

16 yrs. 7 mo

F

Undifferentiated CA

Mediastinum

CP

Y (C)

Pos

NC

No

1 yr 3 Mo

4

7 yrs. 8 mo

M

Undifferentiated CA

Larynx

CP

Y (C)

Negc

NC

No

10 Mo

5

13 yrs. 6 mo

F

Carcinoma

Nasopharynx

CP

Y (E)

ND

?

Yes

 

6

16 yrs. 8 Mo

F

Carcinoma

Lung

CP

Y (C)

Pos

NC

No

8 Mo

7

11 yrs. 8 Mo

M

Carcinoma

Nasopharynx

CP

Y (C)

Neg

NPC

Yes

 

8

5 yrs. 2 Mo

F

Undifferentiated Sarcoma

Retroperitoneum

VAC

Y (C)

Neg

INI neg sarcoma

Yes

 

9

3 yrs. 5 Mo

F

Undifferentiated Sarcoma

Neck

VAC

Y (C)

ND

Probable Rhabdoid

Yes

 

10

13 yrs. 3 Mo

F

Sarcoma

Paraspinal

CP

Y (C)

ND

? MPNST

No

12 Mo

11

14 yrs. 2 Mo

F

Undifferentiated Sarcoma

Paraspinal

VAC

Y (C)

Pos

NC

No

2 yrs. 5 Mo

12

1 yr 2 Mo

M

Undifferentiated Sarcoma

Bladder

VAC

Y (C)

Neg

Rhabdoid

No

1 yr 3 Mo

13

3 yrs. 6 Mo

F

Undifferentiated Sarcoma

Lung

VAC

N

Neg

PPB

No

8 Mo

14

5 Mo

M

Undifferentiated Sarcoma

Neck

VAC

Y (C)

Neg

Probable Rhabdoid

No

6 yrs. 2 Mo

  1. aChemotherapy: (CP) Cisplatinum-based, i.e. Cisplatinum, Doxorubicin, 5FU or Carboplatinum, (Ifos) Ifosfamide, (VAC) Vincristine, Actinomycin and Cyclophosphamide
  2. bRadiotherapy: (Y) yes to primary tumor or (N) no to primary tumor, (E) early with first few cycles or (C) at the end of chemotherapy to consolidate therapy
  3. cProbably technical failure due to fixative
  4. MPNST Malignant peripheral Nerve Sheath Tumor, PPB PleuroPulmonary Blastoma, NPC Nasopharyngeal carcinoma, ND Not determined, CA Carcinoma