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Table 1 Summary of patients with epithelioid hemangioendothelioma treated with anti-angiogenic therapy

From: Pazopanib for metastatic pulmonary epithelioid hemangioendothelioma—a suitable treatment option: case report and review of anti-angiogenic treatment options

First author (ref)

No.pts.

Median age

Gender

Treatment medications

Response

Gaur S [6]

1

35

M

Bevacizumab, Nab-Paclitaxel

SD

Belmont [22]

1

41

M

Bevacizumab, Carboplatin, Paclitaxel

PR

Kim [15]

1

44

F

Bevacizumab, Carboplatin, Paclitaxel

PD

Lopes [16]

1

51

M

Bevacizumab, Carboplatin, Etoposide

PD

Mizota [23]

1

59

F

Bevacizumab, Carboplatin, Paclitaxel

PD

Ye [9]

1

44

F

Bevacizumab, Carboplatin, Paclitaxel

SD

Lazarus [24]

1

42

M

Bevacizumab, Paclitaxel

PD

1

42

M

Carboplatin, Etoposide

PD

Salech [25]

1

40

F

Thalidomide

PR

Raphael et al. [26]

1

53

F

Thalidomide

SD

Kassam et al. [27]

1

13

F

Thalidomide

PD

Bolke et al. [28]

1

47

M

Thalidomide

PD

Mascarenhas et al. [29]

1

52

M

Thalidomide

PR

Pallotti et al. [31]

1

73

M

Lenalidomide

SD

Sumrall et al. [30]

1

31

F

Lenalidomide

SD

Agulnik et al. [18]

2

NA

NA

Bevacizumab

PR

1

NA

NA

Bevacizumab

PD

4

NA

NA

Bevacizumab

SD

Chevreau et al. [19]

5

NA

NA

Sorafenib

SD

2

NA

NA

Sorafenib

PR

8

NA

NA

Sorafenib

PD

  1. PR partial response, PD progressive disease, SD stable disease