No. | Biopsy site | Atypical lymphoid cell size | Phenotype of atypical lymphocytes | TFH markers (#) | CD30 | p53 | CMYC | EBV (Latency) | TCR βF1 | TCRγ gene clonality | Histological diagnosis |
---|---|---|---|---|---|---|---|---|---|---|---|
1 | LN | Large | CD4+ | + (3) | − | + | + | − | + | + | TFH+ PTCL |
2 | Pharynx | Large | CD4+ | + (4) | + | + | − | −* | − | + | TFH+ PTCL |
3 | LN | Large | CD4+ | + (5) | + | + | − | −** | + | − | TFH+ PTCL |
4 | LN | Small | CD4+ | + (4) | − | − | − | −* | − | + | TFH+ PTCL |
5 | LN | Small | CD4+ | + (2) | − | − | − | −* | + | − | TFH+ T-LPDs |
6 | LN | Small | CD4+ | + (2) | − | − | − | −** | + | − | TFH+ T-LPDs |
7 | LN | Small | CD4+ | + (2) | − | − | − | −* | + | − | TFH+ T-LPDs |
8 | LN | Large | CD4+, CD3- | − (0) | + | + | + | + (II) | − | + | PTCL-NOS |
9 | LN | Large | CD4+ | − (0) | + | − | − | + (II) | − | nt | PTCL-NOS |
10 | LN | Small | CD4+ | − (1) | − | − | − | − | + | − | T-LPDs |
11 | LN | Small | CD4+ | − (1) | − | − | − | −* | + | − | T-LPDs |
12 | LN | Large | CD8+ | − (0) | + | + | + | −* | + | nt | systemic ALCL |
13 | Liver | Large | CD8+ | − (1) | + | + | − | + (II) | − | nt | systemic EBV+ TCL of childhood |
14 | BM | Large | CD8+ | − (1) | − | + | + | + (I) | + | + | systemic EBV+ TCL of childhood |
15 | BM, LN | Small | CD8+ | − (1) | ー | − | − | − | + | + | T-LGL |
16 | BM | Small | CD8+ | − (0) | − | − | − | − | + | + | T-LGL |
17 | LN | Small | CD8+ | − (0) | − | − | − | −** | + | + | PTCL-NOS |
18 | BM | Small | CD8+ | − (1) | − | − | − | − | − | nt | HLH |
19 | LN | Small | CD8+ | − (1) | − | − | − | −* | + | − | T-LPDs |
20 | Subcutis | Small | CD8+ | − (1) | − | − | − | − | + | − | Panniculitis-like T-LPDs |
21 | Nose | Large | CD4−, CD8− | − (1) | + | + | + | + (II) | + | + | Nasal type TCL |
Total | na | na | na | 7 | 7 | 8 | 5 | 5 | 15 | 9/17 | na |