Table 1 Modified classification of the central nervous system (CNS) tumors based on the 2016 World Health Organization Classification of Tumors of the CNS [9]
From: Incidence trends of childhood central nervous system tumors in Finland 1990–2017
Tumor group | Morphology code |
|---|---|
(1) Diffuse astrocytic and oligodendroglial tumors | |
Diffuse astrocytomas grade II-III | 9400, 9401 |
Oligodendrogliomas, grade II-III | 9450, 9451 |
Mixed oligo-astrocytoma, grade II-III | 9382 |
Glioblastoma | 9440, 9441 |
Diffuse midline glioma, H3 K27M–mutant | 9385 |
Gliomatosis cerebri (growth pattern) | 9381 |
(2) Other astrocytic tumors (low-grade gliomas) | |
Pilocytic astrocytoma | 9421 |
Pilomyxoid astrocytoma | 9425 |
Subependymal giant-cell astrocytoma | 9384 |
Pleomorphic xanthoastrocytoma | 9424 |
(3) Ependymal tumors | |
Subependymoma | 9383 |
Ependymomas grade II-III | 9391, 9392, 9394 |
Ependymoma, RELA fusion-positive | 9396 |
(4) Neuronal and mixed neuronal-glial tumors | |
Dysembryoplastic neuroepithelial tumor | 9413 |
Gangliocytoma | 9492 |
Ganglioglioma | 9505 |
Dysplastic gangliocytoma of cerebellum | 9493 |
Desmoplastic infantile ganglioglioma | 9412 |
Central neurocytoma | 9506 |
(5) Embryonal tumors | |
Medulloblastoma | 9470, 9471, 9474 |
Central neuroblastoma | 9500 |
Ganglioneuroblastoma | 9490 |
CNS embryonal tumor NOS | 9473 |
Atypical teratoid/rhabdoid tumor | 9508 |
(6) Other tumors | |
Choroid plexus tumors | 9390 |
Other gliomas | 9431, 9430, 9423 |
Tumors of the cranial and paraspinal nerves | 9560, 9540, 9550 |
Meningiomas | 9530, 9537, 9531, 9538, 9539 |
Mesenchymal, non-meningothelial tumors | 9120, 9364, 9150, 8800, 8963, 8990 |
Melanocytic tumors | 8728 |
Germ cell tumors | 9064, 9080, 9084, 9081 |
Malignant glioma NOS | 9380 |
Unclassified tumors | 8000, 8982 |