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Table 1 Percentage of patients diagnosed per specified tumour type

From: Exploring the current status of neuroendocrine tumours: a population-based analysis of epidemiology, management and use of resources

Tumour classification (ICD9-CM)

% of patients

Malignant neuroendocrine tumours (Well- differentiated), (low grade NET) (carcinoid), (intermediate grade NET) (atypical carcinoid), (high grade NET) (atypical carcinoid).

46.86

 209.0 Small intestine

6.95

 209.1 Appendix, large intestine, and rectum

5.05

 209.2 Other and unspecified sites

34.86

  209.20 Unknown primary site

2.46

  209.21 Bronchus and lung

17.34

  209.22 Thymus

0.14

  209.23 Stomach

3.15

  209.24 Kidney

0.27

  209.25 Foregut, not otherwise specified

0.60

  209.26 Midgut, not otherwise specified

2.15

  209.27 Hindgut, not otherwise specified

0.29

  209.29 Other sites not elsewhere classified

8.46

209.3 Malignant poorly differentiated neuroendocrine carcinomas (High grade NEC not otherwise specified), (small cell lung carcinoma), (small cell uterine carcinoma), (small cell neuroendocrine carcinoma), (large cell neuroendocrine carcinoma), (Merkel cell carcinoma).

32.02

 209.30 Malignant poorly differentiated NEC, any site

28.16

 209.31 Merkel carcinoma of the face

1.03

 209.32 Merkel carcinoma of the scalp and neck

0.31

 209.33 Merkel carcinoma of the upper limb

0.56

 209.34 Merkel carcinoma of the lower limb

0.68

 209.35 Merkel carcinoma of the trunk

0.29

 209.36 Merkel carcinoma of the buttock, genitals and others not elsewhere classified

1.00

Benign neuroendocrine tumours (Well- differentiated, (low grade NET) (carcinoid), (intermediate grade NET) (atypical carcinoid).

18.59

 209.4 Small intestine

1.23

 209.5 Appendix, large intestine, and rectum

2.08

 209.6 Other and unspecified sites

15.27

  209.60 Unknown primary site

2.37

  209.61 Bronchus and lung

6.25

  209.62 Thymus

0.04

  209.63 Stomach

1.74

  209.64 Kidney

0.07

  209.65 Foregut, not otherwise specified

0.33

  209.66 Midgut, not otherwise specified

1.07

  209.67 Hindgut, not otherwise specified

0.60

  209.69 Other sites not elsewhere classified

2.80

209.7 Secondary or metastatic neuroendocrine tumours

42.93

 209.70 Unspecified site

0.32

 209.71 Distant lymph nodes

10.32

 209.72 Liver

14.69

 209.73 Bone

4.40

 209.74 Perineum

3.10

 209.75 Secondary Merkel cell carcinoma

0.93

 209.79 Other sites not elsewhere classified

9.17