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Table 2 Therapeutic outcome of CCSK from NWTS studies

From: Clear cell sarcoma of the kidney in a 62-year-old patient presenting with generalized pruritus

Report

Year

Study

n

RFS

EFS

OS

Green [61]

1994

NWTS 1–2 NWTS 3

66

73

25–63.5%(6y) 58.2–64.4%(6y)

NA

NA

25–71.9(6y) 60.8–71.3%(6y)

Seibel [63]

2004

NWST 4

86

65.2–87.8%(5y) 60.6–87.8%(8y)

NA

NA

87.5–95.5%(5y) 85.9–87.5%(8y)

Seibel [64]

2004

NWST 5

110

NA

79%(5y)

89%(5y)

Seibel [65]

2019

NWST 4 NWST 5

68

108

NA

NA

72%(5y) 79%(5y)

87%(5y) 90%(5y)

  1. CCSK clear cell sarcoma of the kidney, NWTS National Wilms Tumor Study, RFS relapse-free survival, EFS event free survival, OS overall survival, NA not available