Report/Year | Age/sex | Symptoms / History | Diagnosis | Ig type | Sites of CSH | Clinical course |
---|---|---|---|---|---|---|
Kaufmann/1996 [5] | 61/F | Subcutaneous masses | G-CSH with LPL in transformation to a large cell lymphoma | IgM kappa IgG lambda | Skin, LN | Not reported |
Jones/1999 [4] | 70/M | Splenomegaly | G-CSH with LPL | IgM kappa | BM, LN | Transformed to DLBCL at 24mos |
Thorson/2000 [7] | 77/F | Bilateral cervical lymphadenopathy | G-CSH with Low-grade monocytoid B-cell lymphoma | lambda | Parotid and submandibular glands, LN | Transformed to DLBCL at 8ys |
Li JJ /2015 [6] | 80/F | Bilateral periorbital swelling | L-CSH with WM | IgM kappa | Skin | Transformed to DLBCL at 6ys and died of disease |
Kawano/2013 [8] | 80/M | Asymptomatic/ Gastric DLBCL 13 years ago(CR) | L-CSH without LP-PCD | None | Lung | Live free of disease at a 23mos follow-up |
Present case | 74/F | Abdominal pain, fever, subcutaneous masses | G-CSH with DLBCL | IgM kappa | Soft tissue, LN | Live with disease at a 1y follow-up |