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Table 4 Incidence and outcome of GISTs from different population-based studies

From: Incidence and clinicopathologic features of gastrointestinal stromal tumors. A population-based study

 

Italy

Sweden [10]

USA [11]

Iceland [12]

Spain [13]

Covered population

     

   Area

Modena

Western Sweden

12 SEER registries

Iceland

Girona

   Population

633,993

1.3–1.6 million

38.7 million

300,000

553,661

   Period

1991–2004

1983–2000

1992–2000

1990–2003

1994–2001

Incidence

     

   Number of cases

124

288

1,458

114

46

   Crude rate#

1.42

1.45

n.a.

n.a.

n.a.

   World ASR#

0.66

n.a.

n.a.

1.1

0.65

   US 2000 ASR#

0.98

n.a.

0.68

n.a.

n.a.

5-years relative survival (%)

     

   All cases

65.8

n.a.

45

n.a.

74.7

   Very low risk

100

n.a.

n.a.

n.a.

94.9(a)

   Low risk

90.1

n.a.

n.a.

n.a.

 

   Intermediate risk

93.1

n.a.

n.a.

n.a.

100

   High risk

61.5(b)

n.a.

n.a.

n.a.

21.4

   Overly malignant

12.4

n.a.

n.a.

n.a.

n.a.

  1. #per 100,000 inhabitants
  2. (a)Very low risk + low risk groups
  3. (b)Excluding overly malignant diseases