From: Prognostic model for predicting overall survival in children and adolescents with rhabdomyosarcoma
All patients | 5 Years OS (%) | 10 Years OS (%) | p | ||||
---|---|---|---|---|---|---|---|
Characteristics | No. | Events | Rate | 95%CI | Rate | 95%CI | |
Entire cohort | 1679 | 543 | 64.5 | 62.1-67.1 | 61.8 | 59.2-64.5 | |
Age (years) | <0.001 | ||||||
0-4 | 639 | 173 | 71.3 | 67.5-75.2 | 69.1 | 65.2-73.2 | |
5-9 | 390 | 97 | 73.2 | 68.5-78.2 | 68.8 | 63.6-74.5 | |
10-14 | 346 | 134 | 56.4 | 50.9-62.6 | 52.4 | 46.6-59.0 | |
15-19 | 304 | 139 | 47.9 | 42.1-54.6 | 47.3 | 41.5-54.0 | |
Tumor size (cm) | <0.001 | ||||||
0-4 | 618 | 116 | 79.5 | 76.0-83.1 | 77.1 | 73.4-81.1 | |
5-9 | 675 | 237 | 61.6 | 57.7-65.7 | 57.6 | 53.5-62.1 | |
≥10 | 386 | 190 | 45.9 | 40.7-51.7 | 44.4 | 39.1-50.3 | |
Sex | 0.311 | ||||||
Male | 974 | 306 | 65.7 | 62.5-69.1 | 62.5 | 59.1-66.1 | |
Female | 705 | 237 | 63.0 | 59.2-67.0 | 60.8 | 56.8-65.0 | |
Race | 0.359 | ||||||
White | 1274 | 407 | 65.2 | 62.4-68.1 | 62.2 | 59.2-65.3 | |
Black | 277 | 88 | 64.0 | 58.0-70.7 | 62.2 | 55.9-69.2 | |
Others | 128 | 48 | 58.7 | 50.0-69.0 | 56.6 | 47.5-67.5 | |
Site | <0.001 | ||||||
Unfavorable | 1026 | 406 | 56.6 | 53.2-59.9 | 53.5 | 50.1-57.1 | |
Favorable | 653 | 137 | 77.1 | 73.6-80.7 | 74.6 | 70.8-78.5 | |
Stage | <0.001 | ||||||
Localized | 561 | 83 | 84.0 | 80.7-87.5 | 81.1 | 77.3-85.1 | |
Regional | 586 | 152 | 72.4 | 68.6-76.5 | 68.5 | 64.3-73.1 | |
Distant | 532 | 308 | 35.7 | 31.5-40.5 | 34.4 | 30.1-39.2 | |
Histology | <0.001 | ||||||
Embryonal | 991 | 249 | 73.5 | 70.6-76.5 | 70.8 | 67.6-74.1 | |
Alveolar | 558 | 263 | 46.3 | 41.9-51.2 | 43.2 | 38.7-48.3 | |
Others | 130 | 31 | 73.1 | 64.9-82.3 | 71.4 | 62.9-81.0 | |
Surgery | <0.001 | ||||||
None | 686 | 294 | 52.0 | 48.0-56.2 | 50.4 | 46.4-54.7 | |
Surgery | 993 | 249 | 73.2 | 70.2-76.3 | 69.9 | 66.3-73.0 | |
Radiotherapy | 0.045 | ||||||
None | 625 | 213 | 62.7 | 58.7-67.0 | 60.8 | 56.6-65.3 | |
Radiation | 1054 | 330 | 65.6 | 62.5-68.9 | 62.3 | 59.1-65.8 |