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Table 1 Patient characteristics at first observation.

From: Chordoma: clinical characteristics, management and prognosis of a case series of 25 patients

Patient characteristics

  

No. (%)

Total number

  

25

Gender

Male

 

18 (72)

 

Female

 

7 (18)

Age (years)

Median: 62

  
 

Range: 40-77

  

Primary tumor site

Sacrum

 

11(44)

 

Spine

 

13(52)

 

Skull base

 

1 (4)

Extension of disease

Primary disease

 

6 (24)

 

Local residual/recurrent disease

14 (56)

 

Metastasis

 

5 (20)

Treatments

Primary surgery

22 (88)

Wide margins

5 (23)

  

Intralesional margins

17 (77)

 

Surgery for recurrent disease

 

13 (52)

 

Radiotherapy

11 (44)

Adjuvant

3 (27)

  

Palliative

8 (73)

 

Target therapy

16 (64)

imatinib meysilate

16

  

nilotinib

1

  

sirolimus

1

 

Chemotherapy plus target therapy

 

1